MRCOG Part 1 Subject Guide

MRCOG Part 1: Genetics

~135 questionsHigh priority

Genetics is one of the four highest-yield subjects in MRCOG Part 1, with approximately 135 questions. Questions are highly specific and formula-driven — particularly around inheritance patterns, recurrence risks and chromosomal disorders. This is a subject where learning the rules pays dividends.

Topics Covered

Mendelian Inheritance

  • Autosomal dominant — 50% recurrence, variable expressivity, incomplete penetrance
  • Autosomal recessive — 25% affected offspring from carrier × carrier cross
  • X-linked recessive — affected males, carrier females (no male-to-male transmission)
  • X-linked dominant — rarer, examples include hypophosphataemia
  • Codominance vs incomplete dominance — blood groups (ABO) as classic example
  • Common AD conditions: Huntington's, achondroplasia, Marfan syndrome, BRCA1/2
  • Common AR conditions: cystic fibrosis, PKU, sickle cell, haemochromatosis

Chromosomal Disorders

  • Trisomy 21 (Down syndrome) — features, risk with maternal age, recurrence risk
  • Trisomy 18 (Edwards) and Trisomy 13 (Patau) — features and prognosis
  • Monosomy X (Turner syndrome) — 45,X, features, fertility implications
  • Klinefelter syndrome (47,XXY) — features, infertility
  • Translocation Down syndrome — 14;21 Robertsonian translocation, recurrence risk calculation
  • Inversions, deletions, microdeletions (22q11 DiGeorge, 5p Cri du Chat)
  • Mosaicism — mitotic error after fertilisation, milder phenotype

Molecular Genetics

  • DNA structure, replication and repair mechanisms
  • Transcription and translation — mRNA, tRNA, codon table
  • Gene mutations — missense, nonsense, frameshift, splice-site
  • DNA repair pathways — BRCA1/2 and homologous recombination
  • Polymerase chain reaction (PCR) — principles and diagnostic applications
  • Southern blot, FISH, array CGH — when each is used clinically

Population Genetics & Screening

  • Hardy-Weinberg equilibrium — allele frequency calculations
  • Carrier frequency calculation from disease incidence
  • Down syndrome screening — first trimester combined (NT + PAPP-A + hCG)
  • NIPT (cell-free fetal DNA) — sensitivity/specificity, what it screens for
  • Imprinting — Prader-Willi (paternal deletion) vs Angelman (maternal deletion)
  • Anticipation — trinucleotide repeats expanding with generations (myotonic dystrophy)

Exam Tips for Genetics

1

Practice risk calculations until they are automatic: recurrence risks for AR (25%), AD (50%), X-linked recessive (50% of sons).

2

Robertsonian translocations: the translocation Down risk depends on which parent carries it — know the carrier-sex difference.

3

Hardy-Weinberg: q² = disease frequency, q = carrier frequency × 2pq. Practice using simple numbers.

4

Imprinting is a guaranteed question type every few sittings — know Prader-Willi vs Angelman and why the same deletion gives different disease.

5

Anticipation and trinucleotide repeats: myotonic dystrophy, Fragile X and Huntington's are the key examples.

Recommended Book

Genetics in Medicine by Thompson & Thompson (8th Edition) — work through methodically.

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